Idiopathic fluctuating hearing loss in right ear with tinnitus but no vertigo

http://m.imgur.com/sLRBYnJ

http://imgur.com/cPXlGXa

-contains two different reports through 2-3 day difference, see the difference in right ear which is effected meanwhile I believe left hearing is like this since childhood except 2007 audio report shows 50 db in left.

Your audiograms show high frequency hearing loss, which is not seen in Meniere's disease, therefore unlikely to be this.  There is no difference between air and bone conduction, therefore it is not Superior Semicircular Canal Dehiscence.  Your high frequency hearing loss is quiet severe.  Did your ENT doctors talk to you about this specific finding?

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

With left almosy pre-deaf, it's hard to spend 5-7 days of ssnhl attack on right ear because as you mentioned I can't even hear high frequency sounds from right ear and it goes like 100 percent deaf but then returns back to normal in 5-7 days max. One specific ent took this as autoimmune and prescribed 24 days prednisone course along with other medications but that reduced the attack gap to about 1-2 weeks.

Other than that they think nerve isnt damaged because hearing is returning back to normal and they're pretty much surprised by this rare condition and have given up.

Can you inform me if you are on any medications?

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

I only started medications after this problem with ents prescribing drugs for cold related problems. Last year I did one week steroid(prednisone)course which reduced gap b/w attacks from 1-2 months to 2 weeks max then after 24 days prednisone se4c 16 and other course gap reduced down to week aometimes two weeks if lucky.

Currently I'm not on any medications

Please allow me a little while to think about your case.

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

Your physician is most likely correct in thinking that this is autoimmune, based also on the audiogram.  The fact that you did not respond to steroids is not because this is wrong, but because this specfic therapy did not work in your case.  You may need to discuss with your physician about whether to be more offensive in the therapy, but the side effects need to be talked about.

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

Did he or she suggest what it is therefore?

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

He referred me to another ENT who's specialist in ear cases after steroid treatment failed. "another ENT" stated he has never encountered such case in his life neither has read or heard about and discarded auto immune with this reason "auto immune comes and stays for month or so then fades away" 

However, I want to add that attacks target certain day over period of time for example through 20-30 days attack comes on Tuesday no matter what, before that target was saturday for several weeks what do you think? 

A quote from one of many scientific publications, important points in CAPITALS:

Eur Arch Otorhinolaryngol. 2009 Jan;266(1):37-40.The diagnosis of autoimmune inner ear disease: evidence and critical pitfalls.Bovo R, Ciorba A, Martini A.

Abstract

The purpose of this paper is to review the current diagnostic work-up for patients with suspected Autoimmune Inner Ear Disease (AIED). AIED is a rare disease accounting for less than 1% of all cases of hearing impairment or dizziness, characterized by a rapidly PROGRESSIVE, often fluctuating, bilateral SNHL over a period of weeks to MONTHS. While specific tests for autoimmunity to the inner ear would be valuable, at the time of writing, there are none that are both commercially available and proven to be useful. Thus far, most of the identified antigens lack a clear association with localized inner ear pathology and the diagnosis of AIED is based either on clinical criteria and/or on a positive response to steroids. For clinical practice, we recommend an antigen-non-specific test battery including blood test for autoimmune disorders and for conditions that resemble autoimmune disorders. Nevertheless, if financial resources are limited, a very restricted work-up study may have a similar efficiency.

Eleftherios S. Papathanasiou, PhD, FEAN

Clinical Neurophysiology

Fellow of the European Academy of Neurology

Negative response or I'd say no response of steroids was the reason for ent to discard auto immune as article states. However can you tell other symptoms and/or several tests to clear this matter.

Constant nightfall, i'm talking sometimes with a day gap and sometimes week. And i think hand-practice sort of triggers attack, not sure about rn but it sure did back year ago. what do you say of it?

and hand practice/nightfall distrubs my ear pressure and triggers tinnitus as well.