Hepatomegaly --> why no info about PLD?

i find this web page very helpful and thorough for many illnesses and symptoms, e.g. Portal Hypertension, Cirrhosis, Budd-Chiari-Syndrom, etc.

As an over 60 yr. patient with PKD and Polycystic Liver Disease (PLD), I am naturally interested in the co-morbidities and symptom descriptions as thoroughly as you have done for many other diseases. In my own case the PKD is in a pre-dialysis stage which means careful monitoring of renal blood values and strict blood pressure control.

The accompanying PLD-Liver is huge and makes for a grossly distended abdomen and through its size has been symptomatic, which puts it in one of those very few percent who are not asymptomatic. The liver has often been aspirated over the last 29 years, de-roofing has been done laparascopically about 20 years ago, and almost 4 years ago exploratory liver surgery, radical fenestration (de-roofing) along with removal of a large section of the liver to reduce the compression of stomach, esophagus and intestines. The gall bladder was removed because histologically shown to have often been inflamed; a hernia was taken care of in the same OP. Portal hypertension and portal vein and hepatic thrombosis (partial) have necessitated permanent anticoagulant treatment.The American PKD web site and perhaps the British web site for PKD fortunately provide quite a bit of helpful information. But judging by your otherwise very thorough and helpful illness descriptions, I would have expected your site to also have included PKD/PLD as a congenital disease with a larger incidence than many more common illnesses.

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